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PXD078968-1

PXD078968 is an original dataset announced via ProteomeXchange.

Dataset Summary
TitleLysoIP-based lysosomal proteomic analysis of WT and mucolipidosis II mouse fibroblasts
DescriptionThis project contains LC–MS/MS-based LysoIP proteomic data from wild-type and mucolipidosis II mouse fibroblasts. The dataset supports the analysis of lysosomal proteome remodeling in a Gnptab p.R364X knock-in mouse model of mucolipidosis II.
HostingRepositoryiProX
AnnounceDate2026-05-28
AnnouncementXMLSubmission_2026-05-28_01:17:29.575.xml
DigitalObjectIdentifier
ReviewLevelPeer-reviewed dataset
DatasetOriginOriginal dataset
RepositorySupportUnsupported dataset by repository
PrimarySubmitterLiang Huan
SpeciesList scientific name: Mus musculus; NCBI TaxID: 10090;
ModificationListNo PTMs are included in the dataset
InstrumentOrbitrap Exploris 240
Dataset History
RevisionDatetimeStatusChangeLog Entry
02026-05-28 01:17:14ID requested
12026-05-28 01:17:30announced
Publication List
Dataset with its publication pending
Keyword List
submitter keyword: LysoIP, mucolipidosis II, Gnptab
Contact List
Huiwen Zhang
contact affiliationPediatric Endocrinology and Genetics, Xinhua Hospital, Shanghai Jiao Tong University School of Medicine, Shanghai Institute for Pediatric Research
contact emailzhanghuiwen@xinhuamed.com.cn
lab head
Liang Huan
contact affiliationXinhua Hospital, Shanghai Jiao Tong University School of Medicine, Shanghai Institute for Pediatric Research
contact emaillh995544@163.com
dataset submitter
Full Dataset Link List
iProX dataset URI